Desmoplastic Infantile Ganglioglioma: A Case Report and Review of the Literature

Authors

  • Eduardo Cambruzzi Federal University of Rio Grande do Sul, Porto Alegre, Rio Grande do Sul, Brazil and Santa Casa Hospital Complex, Porto Alegre, Rio Grande do Sul, Brazil and Conceição Hospital Group, Porto Alegre, Rio Grande do Sul, Brazil and Institute of Cardiology, University Foundation of Cardiology, Porto Alegre, Rio Grande do Sul, Brazil and Unisinos, Faculty of Medicine, São Leopoldo, Rio Grande do Sul, Brazil.
  • Mateus Scarabelot Medeiros Conceição Hospital Group, Porto Alegre, Rio Grande do Sul, Brazil.

DOI:

https://doi.org/10.9734/bpi/rudhr/v1/2790G

Keywords:

Desmoplastic infantile ganglioglioma, central nervous system, childhood brain neoplasm, pathology, prognosis

Abstract

Desmoplastic infantile ganglioglioma (DIG) is a rare glioneuronal tumor characterized by prominent collagen-rich stroma, spindle cell glial component, and small ganglion cells (WHO grade I). The tumor is more frequently identified in the supratentorial region of patients aged less than 1 year with clinical features of macrocephaly or seizures. DIGs are solid-cystic tumors with sharp demarcation from the brain and/or attached to the dura and are associated with a favorable prognosis after complete surgical resection. In this article, we report a case of DIG in a 4-year-old girl presenting with headache, absence seizures, and decreased muscle tone. No clinical signs of recurrence were observed during 8 months of follow-up.

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Published

2024-01-27

How to Cite

Eduardo Cambruzzi, & Mateus Scarabelot Medeiros. (2024). Desmoplastic Infantile Ganglioglioma: A Case Report and Review of the Literature. Recent Updates in Disease and Health Research Vol. 1, 105–117. https://doi.org/10.9734/bpi/rudhr/v1/2790G

Issue

Recent Updates in Disease and Health Research Vol. 1

Section

Chapters