A Novel Approach to Airway Management in Pierre Robin Syndrome with Bicuspid Aortic Valve

Abstract

Pierre Robin Sequence (PRS) is a complex congenital syndrome with a clinical triad of micrognathia, glossoptosis and cleft palate with or without multiple secondary abnormalities leading to the risk of upper airway obstruction and difficulty in feeding. It poses a great challenge to the anaesthesiologist during laryngoscopy and intubation making oxygenation and ventilation difficult. We report a case of 3.5yr male child suffering from PRS along with cleft palate, left renal agenesis, bilateral CTEV, bilateral inguinal hernia, pectus carinatum, bicuspid aortic valve posted for cleft palate repair where successful ventilation and intubation was done and taking a tongue stitch along with nebulization and prone position helped to maintain airway during recovery.