A Brief Study about Dyke Davidoff Masson Syndrome: Rare Cause of Cerebral Hemiatrophy

Authors

  • Amit Vatkar Department of Paediatrics, DY Patil University, School of medicine, Navi Mumbai, Maharashtra, India.
  • Ipsita Vashishtha Department of Paediatrics, DY Patil University, School of medicine, Navi Mumbai, Maharashtra, India.
  • Vinaykumar P. Hedaginal Department of Paediatrics, DY Patil University, School of medicine, Navi Mumbai, Maharashtra, India.
  • B. Revanth Sai Madhav Department of Paediatrics, DY Patil University, School of medicine, Navi Mumbai, Maharashtra, India.

DOI:

https://doi.org/10.9734/bpi/nhmmr/v2/3555E

Keywords:

Dyke-davidoff-masson syndrome, hemiatrophy, spastic hemiplegia, hypoplasia

Abstract

Dyke-Davidoff-Masson syndrome (DDMS) is an uncommon condition, characterized radiologically by cerebral hemiatrophy with homolateral hypertrophy of the skull and sinuses, of unknown frequency resulting from brain injury due to large no of causes; especially in early life. Mostly presents early in life with seizures, learning difficulty, contralateral hemiparesis and facial symmetry. Here we present a case of 11 months old female child with developmental delay, visual abnormality, microcephaly and spastic hemiplegia. CT-brain done which was suggestive of infantile type of cerebral hemiatrophy or DDMS. DDMS is caused by an insult to growing brain either cerebrum in utero when maturation of calvarium has not been completed, or during early life due to damage to brain.

Published

2022-03-08

How to Cite

Amit Vatkar, Ipsita Vashishtha, Vinaykumar P. Hedaginal, & B. Revanth Sai Madhav. (2022). A Brief Study about Dyke Davidoff Masson Syndrome: Rare Cause of Cerebral Hemiatrophy. New Horizons in Medicine and Medical Research Vol. 2, 93–96. https://doi.org/10.9734/bpi/nhmmr/v2/3555E