A Rare Entity on Paediatric RCC with Sarcomatoid Variation
DOI:
https://doi.org/10.9734/bpi/nhmmr/v1/1902BKeywords:
Paediatric RCC, Non-Wilms’ tumours, radical nephrectomy in childrenAbstract
Background: Malignant renal masses in paediatric age group are mostly Wilms’ tumour. RCC is very rare in this age group, papillary variant being the most common. Sarcomatoid variation occurs in 5% of adult RCC, while it is extremely rare in children. No treatment protocol exists in the management of paediatric RCC.
Aims: We present a case of 10-year-old child presenting with an asymptomatic left flank mass.
Case Presentation: Here, we present a case of 10-year-old female who presented with left flank mass. Radi- cal nephrectomy was done which showed clear cell carcinoma with sarcomatoid variant on histopathological examination.
Conclusion: Children can develop RCC with sarcomatoid variant. However, more research and long-term follow-up are required before a therapy strategy and prognostication criteria can be developed.